Citation
J Haem Pract 2016; 3(1):51-54. doi: doi:10.17225/jhp00070

Authors: Chandra Khyati, Mavinakote Gowda Triveni, Rini Gopal, AB Tarunkumar, Suresh Hanagavadi, Dhoom Singh Mehta

Doctor Chandra Khyati
Postgraduate student
Department of Periodontics, Bapuji Dental College and Hospital, Davangere, Karnatka, India.

Doctor Mavinakote Gowda Triveni
Professor
Department of Periodontics, Bapuji Dental College and Hospital, Davangere, Karnatka, India. Email: 2012mgtriveni@gmail.com

Doctor Rini Gopal
Postgraduate student
Department of Periodontics, Bapuji Dental College and Hospital, Davangere, Karnatka, India.

Doctor AB Tarunkumar
Professor
Department of Periodontics, Bapuji Dental College and Hospital, Davangere, Karnatka, India.

Doctor Suresh Hanagavadi
Professor
Department of Pathology and Haematology, JJM Medical College, Davangere, Karnataka, India.

Doctor Dhoom Singh Mehta
Professor and Head
Department of Periodontics, Bapuji Dental College and Hospital, Davangere, Karnatka, India.

Abstract

Haemophilia is a rare blood clotting disorder. Characteristic features of the condition include extemporaneous and post-traumatic subcutaneous bleeding and mucosal haemorrhages.
Genetic deficiency of coagulation factor VIII is the instrumental factor leading to haemophilia A, while deficiency of factor IX leads to haemophilia B. The most common and identified treatment modality for haemophilia A is administration of recombinant or plasma-derived factor VIII concentrate, in order to raise the levels of the deficient factor VIII. Tranexamic acid is also used as an anti-fibrinolytic agent that inhibits plasminogen activators present in oral secretion and stabilises the clot. Administration of factor IX is required in cases of haemophilia B. These treatment modalities lead to the increased longevity and quality of life of the patient. Dental conditions and treatments are more complicated and uncertain in patients with haemophilia due to bleeding risk, thus restorative dental care is of paramount importance for the patient with haemophilia. The fear of bleeding during treatment procedures is the primary cause of lack of proper dental care of people with haemophilia in countries with limited health care resources. This case report highlights the significance of clinical examination and investigation, and the importance of proper interaction between a haematologist and the periodontist for correct multidisciplinary and uneventful management of periodontal health of a patient with haemophilia.

Acknowledgements

This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited

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